Anaesthetic implications in Von Recklinghausen disease: A case report

  • Rosana Guerrero-Domínguez Hospitales Universitarios Virgen del Rocío, Sevilla, Spain
  • Daniel López-Herrera-Rodríguez Hospitales Universitarios Virgen del Rocío, Sevilla, Spain
  • Jesús Acosta-Martínez Hospitales Universitarios Virgen del Rocío, Sevilla, Spain
  • Ignacio Jiménez Hospitales Universitarios Virgen del Rocío, Sevilla, Spain
Keywords: Neurofibroma, Neurofibromatoses, Anesthesia, Airway management, Cafe-au-Lait Spots

Abstract

Von Recklinghausen disease or neurofibromatosis Type I (NF1) is an autosomal dominant disease with a wide spectrum of clinical manifestations. Neurofibromas are the characteristic lesions. This disorder is associated with important anaesthetic considerations, mainly when neurofibromas occur in the oropharynx and larynx, leading to difficult laryngoscopy and tracheal intubation. We describe the anaesthetic management of a patient with NF1 under general anaesthesia for facial neurofibroma excision. We performed a brief review of the literature with the aim of optimizing the anaesthetic management and reducing the number of complications associated with the systemic manifestations of this syndrome.

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How to Cite
1.
Guerrero-Domínguez R, López-Herrera-Rodríguez D, Acosta-Martínez J, Jiménez I. Anaesthetic implications in Von Recklinghausen disease: A case report. Colomb. J. Anesthesiol. [Internet]. 2015Jan.1 [cited 2022Jan.20];43(1):107 -110. Available from: https://www.revcolanest.com.co/index.php/rca/article/view/497

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Published
2015-01-01
How to Cite
1.
Guerrero-Domínguez R, López-Herrera-Rodríguez D, Acosta-Martínez J, Jiménez I. Anaesthetic implications in Von Recklinghausen disease: A case report. Colomb. J. Anesthesiol. [Internet]. 2015Jan.1 [cited 2022Jan.20];43(1):107 -110. Available from: https://www.revcolanest.com.co/index.php/rca/article/view/497
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Case Report / Case Series

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