Orthotopic Liver Transplant in a Patient With Hemophilia A
Abstract
Hemophilia is defined as a recessive hereditary trait linked to the X chromosome. It is characterized by a deficiency of several coagulation factors (hemophilia A: factor VIII, and hemophilia B: factor IX) Clinically, a person with hemophilia has spontaneous bleeding (mostly intra-articular) and the hemostatic control of it is difficult for which the intraoperative management of hemophiliac patients is challenging.
This case report describes a 62 year old patient with hemophilia A, who had a diagnosis of liver cirrhosis secondary to a hepatitis C infection. The patient developed a 22 mm hepatocarcinoma in segment VII of the liver and was successfully subjected to an orthotopic liver transplant at the University Hospital Fundación Santa Fe de Bogotá.
References
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