Orthotopic Liver Transplant in a Patient With Hemophilia A

  • Oswaldo Amaya a Médico anestesiólogo intensivista cardiovascular y de trasplantes, Departamento de Anestesiología del Hospital Universitario Fundación Santa Fe de Bogotá. Profesor asistente de la Universidad El Bosque y de la Universidad de los Andes. Bogotá. Colombia.
  • Juan Andrés Cuervo b Médico anestesiólogo general y de trasplantes, Departamento de Anestesiología del Hospital Universitario Fundación Santa Fe de Bogotá. Bogotá, Colombia.
  • Fernando Raffan c Anestesiólogo general y de trasplantes, intensivista, Departamento de Anestesiología del Hospital Universitario Fundación Santa Fe de Bogotá. Profesor asociado de Anestesiología de la Universidad El Bosque y profesor de cátedra de la Universidad de los Andes. Bogotá, Colombia
  • Fabián Manrique d Médico residente de anestesiología de II año, Departamento Anestesiología del Hospital Universitario Fundación Santa Fe de Bogotá, Universidad El Bosque. Bogotá, Colombia
  • Sergio Martínez e Residente de Anestesiología de I año, Departamento Anestesiología. Hospital Universitario Fundación Santa Fe de Bogotá, Universidad El Bosque. Bogotá, Colombia.
Keywords: Hemophilia A, Liver Transplantation, Trombelastography, Anesthesia, Hepatitis C

Abstract

Hemophilia is defined as a recessive hereditary trait linked to the X chromosome. It is characterized by a deficiency of several coagulation factors (hemophilia A: factor VIII, and hemophilia B: factor IX) Clinically, a person with hemophilia has spontaneous bleeding (mostly intra-articular) and the hemostatic control of it is difficult for which the intraoperative management of hemophiliac patients is challenging.

This case report describes a 62 year old patient with hemophilia A, who had a diagnosis of liver cirrhosis secondary to a hepatitis C infection. The patient developed a 22 mm hepatocarcinoma in segment VII of the liver and was successfully subjected to an orthotopic liver transplant at the University Hospital Fundación Santa Fe de Bogotá.

References

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How to Cite
1.
Amaya O, Cuervo JA, Raffan F, Manrique F, Martínez S. Orthotopic Liver Transplant in a Patient With Hemophilia A. Colomb. J. Anesthesiol. [Internet]. 2011Jan.1 [cited 2021Sep.27];39(1):95-101. Available from: https://www.revcolanest.com.co/index.php/rca/article/view/728

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Published
2011-01-01
How to Cite
1.
Amaya O, Cuervo JA, Raffan F, Manrique F, Martínez S. Orthotopic Liver Transplant in a Patient With Hemophilia A. Colomb. J. Anesthesiol. [Internet]. 2011Jan.1 [cited 2021Sep.27];39(1):95-101. Available from: https://www.revcolanest.com.co/index.php/rca/article/view/728
Section
Case Report / Case Series

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