Thromboelastography as a guide for transfusion therapy in a patient with Turner's syndrome, hypoplasia of the aortic arch and aortic coarctation, undergoing aortoplasty with «sliding technique»: Case report
Keywords:
Aortic coarctation, Thoracic surgery, Thromboelastography, Blood transfusion
Abstract
One of the most frequent lesions in congenital heart disease is hypoplasia of the aortic arch and the co-existence oxf aortic coarctation in older children, which is very difficult to treat. A new technique for treating this condition was recently described and it requires extensive suture lines and an accurate management of coagulation disorders associated with the use of extracorporeal circulation. We present a case of an 8 years and 9 months old girl with Turner's syndrome, aortic coarctation and aortic arch hypoplasia who was admitted for sliding arch aortoplasty and received thromboelastography guided transfusion therapy.
References
1. Thomas J, Yetman A. Management of cardiovascular disease in Turner syndrome. Expert Rev Cardiovasc Ther. 2009;7:1631-1.
2. Douchin S, Rossignol AM, Klein SK, Siché JP, Baguet JP, Bost M. Heart malformations and vascular complications associated with Turner's syndrome. Arch Mai Coeur Vaiss. 2000;93:565-70.
3. Bondy CA. Congenital cardiovascular disease in Turner syndrome. Congenit Heart Dis. 2008;3:2-15.
4. Ravelo HR, Stephenson LW, Friedman S, Chatten J, Rashkind WJ, Vidas M, et al. Coarctation resection in children with Turner's syndrome: a note of caution. J Thorac Cardiovasc Surg. 1980;80:427-30.
5. Badmanaban B, Mole D, Sarsam MA. Descending aortic dissection post coarctation repair in a patient with Turner's syndrome. J Card Surg. 2003;18:153-4.
6. McKenzie D, Klysic M, Morales D. Ascending sliding arch aortoplasty: a novel technique for repair of arch hypoplasia. Ann Thorac Surg. 2011;91:805-10.
7. Brown J, Rodefeld M, Rutzmetov M. Transverse aortic arch obstruction: when to go from the front. Semin Thorac Cardiovasc Surg Pediatr Card Surg Ann. 2009;12:66-9.
8. Shore-Lesserson L, Manspeizer H, DePerio M. Thromboelastography-guided transfusion algorithm reduces transfusions in complex cardiac surgery. Anesth Analg. 1999;88:312-9.
9. Harrison E, Bolton P. Serious Hazards of Transfusion in Children (SHOT). Pediatric Anesthesia. 2011:10-3.
10. Martin P, Horkay F, Rajah SM, Walker DR. Monitoring of coagulation status using thromboelastography during paediatric open heart surgery. Int J Clin Monit Comput. 1991;8:183-7.
11. Williams GD, Bratton SL, Ramamoorthy C. Factors associated with blood loss and blood product transfusions: a multivariate analysis in children after open-heart surgery. Anesth Analg. 1999;89:57-64.
12. Williams GD, Bratton SL, Riley EC, Ramamoorthy C. Coagulation tests during cardiopulmonary bypass correlate with blood loss in children undergoing cardiac surgery. J Cardiothorac Vasc Anesth. 1999;13:398-404.
13. Miller BE, Guzzetta NA, Tosone SR, Levy JH. Rapid evaluation of coagulopathies after cardiopulmonary bypass in children using modified thromboelastography. Anesth Analg. 2000;90:1324-30.
14. Pivalizza EG, Pivalizza PJ, Gottschalk LI, Kee S, Szmuk P, Abramson DC. Celite-activated thrombelastography in children. J Clin Anesth. 2001;13:20-3.
15. Chen A, Teruya J. Global hemostasis testing thromboelastography: old technology new applications. Clin Lab Med. 2009:391-407.
16. Kah-Lok C, Summerhayes R, Ignjatovic V. Reference values for kaolin-activated thromboelastography in healthy children. Anesth Analg. 2007;105:1610-3.
17. Miller B, Guzzetta N, Tosone S. tissue factor activated thromboelastograms in children undergoing cardiac surgery. Anesth Analg. 2003;97:1289-93.
2. Douchin S, Rossignol AM, Klein SK, Siché JP, Baguet JP, Bost M. Heart malformations and vascular complications associated with Turner's syndrome. Arch Mai Coeur Vaiss. 2000;93:565-70.
3. Bondy CA. Congenital cardiovascular disease in Turner syndrome. Congenit Heart Dis. 2008;3:2-15.
4. Ravelo HR, Stephenson LW, Friedman S, Chatten J, Rashkind WJ, Vidas M, et al. Coarctation resection in children with Turner's syndrome: a note of caution. J Thorac Cardiovasc Surg. 1980;80:427-30.
5. Badmanaban B, Mole D, Sarsam MA. Descending aortic dissection post coarctation repair in a patient with Turner's syndrome. J Card Surg. 2003;18:153-4.
6. McKenzie D, Klysic M, Morales D. Ascending sliding arch aortoplasty: a novel technique for repair of arch hypoplasia. Ann Thorac Surg. 2011;91:805-10.
7. Brown J, Rodefeld M, Rutzmetov M. Transverse aortic arch obstruction: when to go from the front. Semin Thorac Cardiovasc Surg Pediatr Card Surg Ann. 2009;12:66-9.
8. Shore-Lesserson L, Manspeizer H, DePerio M. Thromboelastography-guided transfusion algorithm reduces transfusions in complex cardiac surgery. Anesth Analg. 1999;88:312-9.
9. Harrison E, Bolton P. Serious Hazards of Transfusion in Children (SHOT). Pediatric Anesthesia. 2011:10-3.
10. Martin P, Horkay F, Rajah SM, Walker DR. Monitoring of coagulation status using thromboelastography during paediatric open heart surgery. Int J Clin Monit Comput. 1991;8:183-7.
11. Williams GD, Bratton SL, Ramamoorthy C. Factors associated with blood loss and blood product transfusions: a multivariate analysis in children after open-heart surgery. Anesth Analg. 1999;89:57-64.
12. Williams GD, Bratton SL, Riley EC, Ramamoorthy C. Coagulation tests during cardiopulmonary bypass correlate with blood loss in children undergoing cardiac surgery. J Cardiothorac Vasc Anesth. 1999;13:398-404.
13. Miller BE, Guzzetta NA, Tosone SR, Levy JH. Rapid evaluation of coagulopathies after cardiopulmonary bypass in children using modified thromboelastography. Anesth Analg. 2000;90:1324-30.
14. Pivalizza EG, Pivalizza PJ, Gottschalk LI, Kee S, Szmuk P, Abramson DC. Celite-activated thrombelastography in children. J Clin Anesth. 2001;13:20-3.
15. Chen A, Teruya J. Global hemostasis testing thromboelastography: old technology new applications. Clin Lab Med. 2009:391-407.
16. Kah-Lok C, Summerhayes R, Ignjatovic V. Reference values for kaolin-activated thromboelastography in healthy children. Anesth Analg. 2007;105:1610-3.
17. Miller B, Guzzetta N, Tosone S. tissue factor activated thromboelastograms in children undergoing cardiac surgery. Anesth Analg. 2003;97:1289-93.
How to Cite
1.
Pérez Pradilla AC, Tamariz-Cruz O, Motta Amézquita LG, Barrera Fuentes M, Palacios Macedo Quenot A. Thromboelastography as a guide for transfusion therapy in a patient with Turner’s syndrome, hypoplasia of the aortic arch and aortic coarctation, undergoing aortoplasty with «sliding technique»: Case report. Colomb. J. Anesthesiol. [Internet]. 2012 Oct. 1 [cited 2024 Apr. 25];40(4):318–322. Available from: https://www.revcolanest.com.co/index.php/rca/article/view/781
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Published
2012-10-01
How to Cite
1.
Pérez Pradilla AC, Tamariz-Cruz O, Motta Amézquita LG, Barrera Fuentes M, Palacios Macedo Quenot A. Thromboelastography as a guide for transfusion therapy in a patient with Turner’s syndrome, hypoplasia of the aortic arch and aortic coarctation, undergoing aortoplasty with «sliding technique»: Case report. Colomb. J. Anesthesiol. [Internet]. 2012 Oct. 1 [cited 2024 Apr. 25];40(4):318–322. Available from: https://www.revcolanest.com.co/index.php/rca/article/view/781
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Section
Case Report / Case Series
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