TY - JOUR AU - Lippi Quiñones, Angelina AU - López Jaque, Nathalie AU - Maureira Moreno, Verónica PY - 2022/12/15 Y2 - 2024/03/29 TI - Escobar syndrome, difficult airway management in pediatrics: A case report JF - Colombian Journal of Anesthesiology JA - Colomb. J. Anesthesiol. VL - 51 IS - 1 SE - Case Report / Case Series DO - 10.5554/22562087.e1057 UR - https://www.revcolanest.com.co/index.php/rca/article/view/1057 SP - AB - <p>Escobar syndrome is a rare, autosomal recessive disease of unknown incidence. It is characterized by multiple skeletal, genitourinary and orofacial abnormalities. The multiple malformations (mainly orofacial) and restricted mobility of these patients pose a challenge to the anesthesia team, especially as regards airway management. We describe the clinical case of a pediatric patient diagnosed with Escobar syndrome who underwent two consecutive anesthesia interventions, with evidence of progressive airway anomalies that characterize this syndrome. &nbsp;The case required adaptation, according to the clinical stage of the disease, of the current algorithms used to approach an anticipated difficult airway in pediatrics, &nbsp;and&nbsp; the incorporation of new devices, not described so far in patients with this pathology, as part of the planning and execution phases.</p> ER -