Anesthetic implications of Parry Romberg Syndrome: A case report

  • Guiomar Fernández-Castellano Hospitales Universitarios Virgen del Rocío, Seville, Spain
  • Rosana Guerrero-Domínguez Hospitales Universitarios Virgen del Rocío, Seville, Spain
  • Daniel López-Herrera-Rodríguez Hospitales Universitarios Virgen del Rocío, Seville, Spain
  • Ignacio Jiménez Clinical Management Unit for Anesthesiology and Reanimation, Hospital for Traumatology and Rehabilitation, Hospitales Universitarios Virgen del Rocío, Seville, Spain
Keywords: Laryngoscopy, Anesthesia, Airway management, Facial hemiatrophy, Craniofacial dysostosis

Abstract

Introduction: Parry-Romberg Syndrome is a rare degenerative disease characterized by unilateral atrophy affecting the skin, connective tissue, muscle and bone. The end result is facial asymmetry associated with other skin, dental, visual, cardiovascular, and neurological disorders.

Clinical findings, diagnostic evaluation and interventions: The case of a patient with Parry-Romberg Syndrome programmed for frontonasal flap remodeling is discussed. The patient's history includes trigeminal neuralgia, epilepsy, and two previous surgical interventions. Uneventful endotracheal intubation with the Glideoscope® video laryngoscope was performed, upon adequate pre-oxygenation followed by anesthetic induction.

Conclusion: The phenotypical characteristics of Parry Romberg Syndrome are severe facial hemiatrophy and craniofacial anomalies that require careful preoperative evaluation and management of a potentially difficult airway. Consequently, the use of video laryngoscopes is a first-line approach. Due to the syndrome's associated disorders, it is essential to maintain hemodynamic stability and prevent any potential seizures.

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How to Cite
1.
Fernández-Castellano G, Guerrero-Domínguez R, López-Herrera-Rodríguez D, Jiménez I. Anesthetic implications of Parry Romberg Syndrome: A case report. Colomb. J. Anesthesiol. [Internet]. 2017Apr.1 [cited 2021Dec.5];45(Supplement):26 -30. Available from: https://www.revcolanest.com.co/index.php/rca/article/view/445

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Published
2017-04-01
How to Cite
1.
Fernández-Castellano G, Guerrero-Domínguez R, López-Herrera-Rodríguez D, Jiménez I. Anesthetic implications of Parry Romberg Syndrome: A case report. Colomb. J. Anesthesiol. [Internet]. 2017Apr.1 [cited 2021Dec.5];45(Supplement):26 -30. Available from: https://www.revcolanest.com.co/index.php/rca/article/view/445
Section
Case Report / Case Series

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